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TORSION OF A WANDERING SPLEEN IN AN ADOLESCENT WITH GAUCHER DISEASE

ŞÜKRÜ GÜNGÖR, MEHMET ÖZTÜRK, FATMA İLKNUR VAROL, AHMET SIĞIRCI, MUKADDER AYŞE SELİMOĞLU

The Turkish Journal of Gastroenterology - 2017;28(4):303-306

Department of Pediatric Gastoenterology, İnönü University School of Medicine, Malatya, Turkey

 

A wandering spleen is a rare condition characterized by the malposition of the spleen due to laxity or absence of its supporting ligaments. Although Gaucher disease generally presents with massive splenomegaly, which one of the predisposing causes of a wandering spleen, literature shows only one report of a wandering spleen in a child with Gaucher disease. In this case presentation, a 13-year-oldadolescent with Gaucher disease on enzyme replacement treatment was presented, who was detected having an abdominal mass on a routine visit and diagnosed with partial torsion of a wandering spleen associated with left lobe hypoplasia of the liver.