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A RARE CASE OF MIDAORTIC SYNDROME: VASCULAR BEHÇET'S DISEASE OR TAKAYASU ARTERITIS?

Zeynep Ece DEMİRBAŞ, Abdullah Kemal TUYGUN

Türk Göğüs Kalp Damar Cerrahisi Dergisi - 2026;34(2):172-174

Department of Internal Medicine, University of Health Sciences Türkiye, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Türkiye

 

This case report describes a 44-year-old man with midaortic syndrome and resistant hypertension, presenting a diagnostic challenge due to overlapping features of Behçet's disease and Takayasu arteritis. Imaging studies revealed severe aortic stenosis accompanied by aortic wall thickening, findings typically associated with Takayasu arteritis; however, the patient's clinical history and a positive pathergy test supported a diagnosis of Behçet's disease. Immunosuppressive therapy led to symptomatic improvement, and surgical management with thoracic endovascular aortic repair was successfully performed to address the aortic stenosis. This report discusses the possibility of Behçet's disease presenting with aortic stenosis-a rare vascular complication-or the coexistence of Behçet's disease and Takayasu arteritis.