FATMA TUBA COŞKUN, MELTEM UGRAS, ENDİ ROMANO, MERT LEVENT BARUT, ERCAN KOCAKOÇ
Yeditepe Tıp Dergisi - 2016;12(37-38):989-992
Konjenital ekstrahepatik portosistemik şant (Abernethy malformasyonu) çok nadir görülen bir bozukluktur. It is classified into two types based on the pattern of anastomosis between the portal vein(PV) and inferior vena cava(IVC), and the presence or absence of an intrahepatic portal venous supply. Patients with Abernethy malformations have cardiac and hepatic abnormalities. It rarely can lead to hepatocellular carcinoma in the long term. Here we report a 16- years- old girl who is diagnosed as Abernethy malformation as a result of investigations of early puberty
