AN EXTREMELY RARE CAUSE OF WOLFF-PARKINSON-WHITE SYNDROME: RHABDOMYOMA IN ASSOCIATION WITH TUBEROUS SCLEROSIS

ÖZLEM ELKIRAN, CEMŞİT KARAKURT, DAMLA İNCE

Journal of Clinical Practice and Research - 2019;41(1):108-110

Department of Pediatric Cardiology, İnonu University Faculty of Medicine, Malatya, Turkey

 

Rhabdomyomas are the most common primary cardiac tumors in infants and children. They are usually associated with tuberous sclerosis (TS). As the tumors tend to regress spontaneously, surgical intervention is not usually performed unless they become obstructive or cause incessant arrhythmias. We report an extremely rare case of rhabdomyoma serving as a substrate for Wolff-Parkinson-White (WPW) syndrome and intractable supraventricular tachycardia accompanied by TS. Our case is particularly interesting because it was diagnosed prenatally. The signs of WPW syndrome disappeared from the electrocardiogram with the regression of the tumor.