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ADR Yönetimi
ADR Yönetimi

EFFECT OF LARGE NEUTRAL AMINO ACIDS TREATMENT ON BLOOD PHENYLALANINE, TYROSINE, AND TRYPTOPHAN LEVELS IN ADOLESCENT AND YOUNG ADULT PKU PATIENTS

FEHİME ERDEM, EBRU CANDA, HAVVA YAZICI, YASEMİN ATİK ALTINOK, MERVE YOLDAŞ ÇELİK, AYŞE YÜKSEL YANBOLU, SEMA KALKAN UÇAR, SARA HABİF, MAHMUT ÇOKER

Trends in Pediatrics - 2025;6(2):82-88

Division of Pediatrics Metabolism and Nutrition, Department of Pediatrics, Faculty of Medicine, Ege University, İzmir, Türkiye

 

Objective: We aimed to evaluate the change in phenylalanine (Phe), Tyrosine (Tyr), and Tryptophan (Trp) blood levels in classical PKU patients treated with large neutral amino acids (LNAA) supplementation.