Hayriye Zehra TÜRK, Ebru AKLEYİN, Betül SÜLÜ
Journal of Dental Sciences and Education - 2026;4(2):70-75
Smith-Magenis syndrome (SMS) is a rare, genetically-based syndrome affecting multiple systems. It is characterized by developmental delay, behavioral disorders, and characteristic facial features. While various descriptions of the craniofacial and oral findings of SMS exist in the literature, studies involving dental treatment requirements are quite limited. This study aims to present the oral and dental rehabilitation performed for the second time under general anesthesia in a 9-year-old pediatric patient diagnosed with SMS during the mixed dentition period, who presented to our clinic with pain complaints, and to discuss the challenges of dental management of this rare syndrome in light of the literature.
