PAPILLARY INTRALYMPHATIC ANGIOENDOTHELIOMA: AN EXTREMELY RARE TUMOR

GÜVEN OZAN KAPLAN, FETHİYE DAMLA MENKU ÖZDEMİR, DİCLEHAN ORHAN, ALİ EMRE AKSU, FİGEN ÖZGÜR

Joint Diseases and Related Surgery - 2021;32(1):245-248

Department of Plastic, Reconstructive and Aesthetic Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey

 

Papillary intralymphatic angioendothelioma (PILA), an intralymphatic lesion of vascular ducts, is an extremely rare tumor. It is generally encountered as an unexpected pathology following excision of a vascular skin lesion. Re-excision is the commonly preferred treatment option once the pathological diagnosis is established. In this article, we present a 12-year-old male patient with a PILA treated with re-excision, skin grafting, and sentinel lymph node biopsy. The patient was symptom-free at annual follow-up. A sentinel lymph node biopsy during re-excision might be a good option in the surgical management of PILA. Frequent examination of lymph nodes and skin lesion also might be beneficial during the follow-ups.