NADER SHAKİBAZAD, KARMELLA KAMALİ, NASER HONAR, MOHAMMADREZA BORDBAR, ERFANEH MOHAZABİEH
Experimental and Clinical Transplantation - 2018;16(3):352-354
Rigler sign is a double wall sign suggesting pneu - moperitoneum and intestinal perforation, and it needs emergency surgical treatment. Early diagnosis of intestinal perforation by clinical symptoms, presence of Rigler sign in abdominal radiography, and then early surgical treatment can reduce mortality. Here, we report a patient with Crigler-Najjar syndrome who underwent liver transplant and then developed posttransplant lymphoproliferative disease and received chemotherapy with cyclophosphamide, doxorubicin, vincristine, and prednisone plus ritux - imab. She was referred to the emergency department due to abdominal distension with positive Rigler sign in abdominal radiography; intraoperative findings revealed intestinal perforation. Pediatricians and surgeons should be aware of Rigler sign so that it is diagnosed early and emergency surgical treatment can be performed.
