Büşra Nur ÖZCAN ERİŞGİN, Bedirhan ALBAYRAK, Altan AKSU, Mennan Ece PİRZİRENLİ, Ahmet UZUN, Sena KAMALI KURNAZ, Hüseyin Sina COŞKUN
Journal of Experimental and Clinical Medicine - 2026;43(2):257-260
Sprengel deformity is a rare congenital anomaly resulting from failed caudal migration of the scapula during embryonic development. In selected patients, an omovertebral bone may forms a rigid osseous tether between the cervical spine and scapula, restricting scapulothoracic motion and contributing substantially to functionl impairment. We report the case of an 8-year-old girl with left-sided Cavendish grade III Sprengel deformity who presented with limited shoulder elevation and a well-corticated omovertebral bone extending from the C4 spinous process to the superomedial scapular angle. Computured tomography provided detailed visulization of the morphology, orientation, thereby facilitating precise surgical planning. The patient underwent targeted posterior excision of the osseous tether without intraoperative or postoperative complications. At the six-month follow-up, marked improvement in shoulder elevation, enhanced scapular symmetry, and excellent cosmetic and functional recovery were observed. This case underscores the mechanical significance of the omovertebral bone in Sprengel deformity and supports anatomy-guided isolated excision as an effective treatment option in carefully selected pediatric patients in whom the deformity is predominantly driven by a discrete osseous connection.
