Paddy DEWAN, Padma RAO, Mandar Massada da ROCHA, Renata DHIRAJLAL, Adalberto Clemente BOCA
Pediatric Urology Case Reports - 2026;13(2):733-737
The multicystic dysplastic kidney is now understood to be due to the combination of a vascular accident to both the ureteric bud and the renal blastema resulting in a characteristic appearance, but with wide variation possible. We present the case of a girl with evidence of the prenatal loss of blood supply of her only functioning kidney, which may be the only such case recorded, as the other two cases recorded may well not have the same aetiology because the morphology appeared to differ from the asserted embryopathy. The surgery required in our case differed from a normal pyeloplasty (for the pelviureteric junction obstruction component of the uropathy) to ensure the remaining blood supply to the minimal parenchyma was not compromised.
