TERATOID WILMS TUMOR: REPORT OF THREE CASES AND REVIEW OF THE LITERATURE

DOAA AL GHAMDI, NASİR BAKSHI, MOHAMMED AKHTAR

Türk Patoloji Dergisi - 2019;35(1):61-68

Department of Pathology and Laboratory Medicine, King Faisal Specialist Hospital and Research Centre, RIYADH, SAUDI ARABIA

 

Teratoid Wilms tumor is a rare variant of Wilms tumor composed predominantly of well-differentiated epithelial and/or mesenchymal heterologous elements. Like the classical Wilms tumor, this variant may also occur as a renal mass or may be found in extra renal locations. This tumor may be treated effectively by surgical resection; however, it generally fails to respond to chemotherapy. A review of the literature revealed 30 reported cases of intra renal and 5 reports of extra renal teratoid Wilms tumor. We report our experience with an additional three cases of renal teratoid Wilms tumor adding to the 30 cases previously reported.