Ege Karslıoğlu, Almila Sarıgül Sezenöz, Gürsel Yılmaz
Türk Oftalmoloji Dergisi - 2026;56(3):208-210
Retinal venous beading is a rare retinal vascular anomaly characterized by segmental dilatation of the retinal veins. It is typically associated with systemic or ocular disorders such as hypertension, diabetes or central retinal vein occlusion (CRVO). Idiopathic retinal venous beading is exceedingly uncommon, especially unilateral presentations, and may serve as a clinical indicator of systemic disorders, particularly renal or metabolic diseases such as Fabry and Alport syndromes. This report presents a rare case of unilateral idiopathic retinal venous beading, outlines its differential diagnosis, and discusses potential pathophysiological mechanisms.